X-linked hypohidrotic ectodermal dysplasia management with removable prosthesis in a pediatric patient. Case Report.

Héctor Rodríguez; José Rodríguez; Maria Acosta de Camargo; Hazel Topel; Miguel Hirschhaut

doi:10.17126/joralres.2022.055

Héctor Rodríguez Javeriana University, Bogota, Colombia
José Rodríguez Centro de Estudios Superiores en Ortodoncia, Mexico City, Mexico
Maria Acosta de Camargo University of Carabobo. Department of Pediatric Dentistry, Valencia, Venezuela http://orcid.org/0000-0001-7615-918X
Hazel Topel Javeriana University, Bogota, Colombia
Miguel Hirschhaut Policlínica Americana, Caracas, Venezuela http://orcid.org/0000-0002-3972-8619

DOI: https://doi.org/10.17126/joralres.2022.055

Abstract

Introduction: Ectodermal dysplasia is a rare genetic disorder that affects structures derived from ectoderm such as teeth, hair, nails, and sweat glands. Oligodontia is a common finding that affects the chewing, smiling and self- esteem of these pediatric patients.
Case Report: We present a case report of a 7-years-old pediatric patient who consulted with his mother, showing the same condition. The intervention consisted of a removable prosthesis with satisfactory results.
Conclusion: The X-linked hypohidrotic ectodermal dysplasia represents a challenge for a pediatric dentist who offers rehabilitation to the patient according to craniofacial development, age, socioeconomic status, and the number of missing teeth.

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