Pierre Robin Sequence: airway management via mandibular distraction. Case report.

  • Hernán Arango Fernández Servicio de Cirugía Oral y Maxilofacial, Fundación Hospital Universitario Metropolitano. Barranquilla, Colombia.
  • Martha Rebolledo Cobos Departamento de Cirugía Oral, Universidad Metropolitana. Labo-ratorio de Genética Molecular, Universidad Simón Bolívar. Barranquilla, Colombia.
  • Saulo Pineda Ovalle Servicio de Cirugía Oral y Maxilofacial, Fundación Hospital Universitario Metropolitano. Barranquilla, Colombia.
  • Jonathan Harris Ricardo Departamento de Medicina Oral, Clí-nica Odontológica de la Corporación Universitaria Rafael Núñez. Cartagena, Colombia.

Abstract

Pierre Robin sequence is a set of congenital conditions characterized by the presence of micrognathia, glossoptosis, cleft palate and obstruction of the airways. The latter can lead to many other complications such as respiratory difficulties, apnea, weight loss and even death. Currently, mandibular distraction, or the lengthening of the mandibular bone, is the most common surgical procedure used to correct a retracted tongue and the airway obstruction it produces in patients with mandibular hypoplasia. The present paper reports the case of a 26-day-old male patient, who presented obstruction on the upper respiratory tract, mandibular retromicrognathia, and retracted tongue and cleft palate, all conditions characteristic to Pierre Robin sequence. The patient also had a medical record of orotracheal intubation due to respiratory difficulties. The subject underwent mandibular distraction surgery with a horizontal vector, which resulted in a satisfactorily cleared airway. 

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Published
2019-07-18
How to Cite
ARANGO FERNÁNDEZ, Hernán et al. Pierre Robin Sequence: airway management via mandibular distraction. Case report.. Journal of Oral Research, [S.l.], v. 8, n. 3, p. 244-248, july 2019. ISSN 0719-2479. Available at: <http://joralres.com/index.php/JOR/article/view/818>. Date accessed: 17 sep. 2019. doi: https://doi.org/10.17126/jor.v0i0.818.
Section
Cases